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KD-Validated ALAS2 Recombinant Rabbit Monoclonal Antibody
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KD-Validated ALAS2 Recombinant Rabbit Monoclonal Antibody

KVAb01222-50ul · 50ul

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Catalog No: KVAb01222-50ul
Pack Size: 50ul
Brand: EnkiLife

Description

EnkiLife offers the KD-Validated ALAS2 Recombinant Rabbit Monoclonal Antibody. This antibody reacts with Human,Mouse,Rat and is suitable for WB,FCM application. The product boasts remarkable high specificity, outstanding reproducibility, and exceptional affinity, making it a reliable and superior choice for your needs. Dilution Ratio: WB 1:1,000-1:5,000; FC 1:200-1:2,000 Alternative Names of Immunogen:ALAS2; 5'-Aminolevulinate Synthase 2; ALAS-E; ASB; 5-Aminolevulinate Synthase, Erythroid-Specific, Mitochondrial; Erythroid-Specific Delta-Aminolevulinate Synthase; Aminolevulinate, Delta-, Synthase 2; 5-Aminolevulinic Acid Synthase 2; Delta-Aminolevulinate Synthase 2; Delta-ALA Synthase 2; EC 2.3.1.37; ALASE; Aminolevulinate, Delta-, Synthase 2 (Sideroblastic/Hypochromic Anemia); Sideroblastic/Hypochromic Anemia; Delta-ALA Synthetase; SIDBA1; XLDPP; XLEPP; ANH1; XLSA Background: The product of this gene specifies an erythroid-specific mitochondrially located enzyme. The encoded protein catalyzes the first step in the heme biosynthetic pathway. Defects in this gene cause X-linked pyridoxine-responsive sideroblastic anemia. Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq, Jul 2008] Research Area: Cardiovascular,Signal Transduction,Cancer,Metabolism

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