KD-Validated GBE1 Mouse Monoclonal Antibody

Description

EnkiLife offers the KD-Validated GBE1 Mouse Monoclonal Antibody. This antibody reacts with Human and is suitable for WB,FCM,ICC application. The product boasts remarkable high specificity, outstanding reproducibility, and exceptional affinity, making it a reliable and superior choice for your needs. Dilution Ratio: WB 1:500-1:2,500; FC 1:100-1:1,000; ICC 1:100-1:1,000 Alternative Names of Immunogen:GBE1; 1,4-Alpha-Glucan Branching Enzyme 1; Glucan (1,4-Alpha-), Branching Enzyme 1; 1,4-Alpha-Glucan-Branching Enzyme; Glycogen Branching Enzyme; Brancher Enzyme; EC 2.4.1.18; Amylo-(1,4 To 1,6) Transglucosidase; Amylo-(1,4 To 1,6) Transglycosylase; Glycogen Storage Disease Type IV; Glycogen-Branching Enzyme; Andersen Disease; APBD; GSD4; GBE Background: The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease). [provided by RefSeq, Jul 2008] Research Area: Signal Transduction,Cancer,Metabolism