KD-Validated PCCA Mouse Monoclonal Antibody

Description

EnkiLife offers the KD-Validated PCCA Mouse Monoclonal Antibody. This antibody reacts with Human,Mouse,Rat and is suitable for WB,ICC application. The product boasts remarkable high specificity, outstanding reproducibility, and exceptional affinity, making it a reliable and superior choice for your needs. Dilution Ratio: WB 1:500-1:2,500; ICC 1:100-1:1,000 Alternative Names of Immunogen:PCCA; Propionyl-CoA Carboxylase Subunit Alpha; Propionyl-CoA Carboxylase Alpha Chain, Mitochondrial; Propionyl Coenzyme A Carboxylase, Alpha Polypeptide; EC 6.4.1.3; Propanoyl-CoA:Carbon Dioxide Ligase Alpha Subunit; Propanoyl-CoA:Carbon Dioxide Ligase Subunit Alpha; Propionyl CoA Carboxylase, Alpha Polypeptide; Propionyl-CoA Carboxylase Alpha Subunit; PccA Complementation Group; PCCase Alpha Subunit; PCCase Subunit Alpha; EC 6.4.1 Background: The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, May 2010] Research Area: Signal Transduction,Metabolism